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Al-Benna S, Hasler R, Stricker I, et al. Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report. Cases J. 2009;2:7067doi: 10.4076/1757-1626-2-7067.
Al-Benna, S., Hasler, R., Stricker, I., Steinau, H. U., & Steinstraesser, L. (2009). Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report. Cases journal, 27067. https://doi.org/10.4076/1757-1626-2-7067
Al-Benna, Sammy, et al. "Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report." Cases journal vol. 2 (2009): 7067. doi: https://doi.org/10.4076/1757-1626-2-7067
Al-Benna S, Hasler R, Stricker I, Steinau HU, Steinstraesser L. Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report. Cases J. 2009 Aug 28;2:7067. doi: 10.4076/1757-1626-2-7067. PMID: 19918506; PMCID: PMC2769336.
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Cases J. 2009 Aug 28;2:7067. doi: 10.4076/1757-1626-2-7067.

Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report.

Cases journal

Sammy Al-Benna, Raphael Hasler, Ingo Stricker, Hans-Ulrich Steinau, Lars Steinstraesser

Affiliations

  1. Department of Plastic and Reconstructive Surgery, Department of Hand Surgery, Soft Tissue Tumour Reference Centre, BG University Hospital Bergmannsheil, Ruhr University Bochum, Buerkle-de-la Camp-Platz 1, 44789 Bochum, Germany. [email protected]

PMID: 19918506 PMCID: PMC2769336 DOI: 10.4076/1757-1626-2-7067

Abstract

Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old German Caucasian male with Papillon-Lefèvre syndrome associated with recurrent squamous cell carcinoma. Treatment is symptomatic and not always satisfactory.

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