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Eur J Dent. 2010 Apr;4(2):215-22.

Ectodermal dysplasia with anodontia: a report of two cases.

European journal of dentistry

Mehmet Bani, Ali Melih Tezkirecioglu, Nese Akal, Tamer Tuzuner

Affiliations

  1. DDS, Research Assistant, Gazi University, Faculty of Dentistry, Department of Paediatric Dentistry, Ankara, Turkey.

PMID: 20396456 PMCID: PMC2853819

Abstract

Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances in the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. Two case reports illustrating the prosthetic rehabilitation of 2 young boys with anhidrotic ectodermal dysplasia associated with severe anodontia are presented. Since the oral rehabilitation of these cases is often difficult; particularly in pediatric patients, treatment should be administered by a multidisciplinary team involving pediatric dentistry, orthodontics, prosthodontics and oral-maxillofacial surgery.

Keywords: Anodontia; Ectodermal dysplasia; Multidisciplinary management; Prosthetic rehabilitation

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