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Grech V, Grixti C. Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report. J Med Case Rep. 2010;4:168doi: 10.1186/1752-1947-4-168.
Grech, V., & Grixti, C. (2010). Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report. Journal of medical case reports, 4168. https://doi.org/10.1186/1752-1947-4-168
Grech, Victor, and Grixti, Cynthia. "Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report." Journal of medical case reports vol. 4 (2010): 168. doi: https://doi.org/10.1186/1752-1947-4-168
Grech V, Grixti C. Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report. J Med Case Rep. 2010 Jun 02;4:168. doi: 10.1186/1752-1947-4-168. PMID: 20525186; PMCID: PMC2894860.
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J Med Case Rep. 2010 Jun 02;4:168. doi: 10.1186/1752-1947-4-168.

Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report.

Journal of medical case reports

Victor Grech, Cynthia Grixti

Affiliations

  1. Paediatric Department, Mater Dei Hospital, Disneyland, Tal-Qroqq, Malta. [email protected].

PMID: 20525186 PMCID: PMC2894860 DOI: 10.1186/1752-1947-4-168

Abstract

INTRODUCTION: Disconnected pulmonary arteries are unusual and may result in pulmonary hypertension with acute right heart failure.

CASE PRESENTATION: We report a case of a three-month-old Asian girl who presented with heart failure and severe pulmonary hypertension due to a disconnected right pulmonary artery. An epoprostenol (prostacyclin) infusion was instrumental in lowering pulmonary artery pressures and stabilizing the child prior to surgery.

CONCLUSIONS: This is, to the best of our knowledge, the first report of successful prostacyclin usage in such a situation.

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