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Hand (N Y). 2011 Jun;6(2):217-9. doi: 10.1007/s11552-010-9309-1. Epub 2010 Nov 19.

Hand involvement in Navajo neurohepatopathy: a case report.

Hand (New York, N.Y.)

Tahseen A Cheema, Scott Swanson

Affiliations

  1. Division of Hand Surgery, Department of Orthopaedic Surgery, MSC10 5600, 1 University of New Mexico, Albuquerque, NM 87131-0001 USA.

PMID: 22654708 PMCID: PMC3092889 DOI: 10.1007/s11552-010-9309-1

Abstract

We report a case of Navajo neurohepatopathy with severe involvement of the hands. It is a progressive sensorimotor neuropathy with distal weakness, areflexia, and reduced sensation in the extremities associated with acral mutilation. The role of possible surgical intervention is demonstrated in this case.

Keywords: Hereditary peripheral neuropathy; Intrinsic paralysis; Navaho neurohepatopathy

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