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Indian J Otolaryngol Head Neck Surg. 2007 Sep;59(3):273-6. doi: 10.1007/s12070-007-0079-1. Epub 2007 Oct 05.

Primary extraskeletal Ewing's sarcoma of the maxilla with intraorbital extension.

Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of India

Saurabh Varshney, S S Bist, Nitin Gupta, Rajat Bhatia

Affiliations

  1. Department of E.N.T., Himalayan Institute of Medical Sciences, Jollygrant; Doiwala Dehradun, 248 140 Uttaranchal India.

PMID: 23120451 PMCID: PMC3452126 DOI: 10.1007/s12070-007-0079-1

Abstract

Extraskeletal Ewing's sarcoma is often described as a tumour involving the soft tissues of the lower extremities and the paravertebral region. Primary Ewing's sarcoma of the cranium is extremely rare, with only 17 cases reported so far [24]. Involvement of the paranasal sinus is a very rare entity. Involvement of facial bones is characterized by clinical and radiological features distinct from those commonly observed in other sites. Because of the above peculiarities a delay in diagnosis and thus in starting treatment is very probable in such cases. Primary Ewings sarcoma rarely arises in the facial skeleton and only occasionally in the maxilla. To date, there have been 22 cases of maxillary Ewing's sarcoma reported in the English-language literature [25]. We report here a new case of Ewing's sarcoma localized to the maxillary sinus, nose and the orbit, successfully treated by surgery, local high dosage radiotherapy and systemic chemotherapy.

Keywords: Ewing’s sarcoma; Paranasal sinus

References

  1. Am J Clin Pathol. 1981 Mar;75(3):410-5 - PubMed
  2. Br J Neurosurg. 1993;7(6):683-6 - PubMed
  3. J Laryngol Otol. 1978 Nov;92(11):1007-24 - PubMed
  4. Cancer Lett. 1996 Jun 5;103(2):177-82 - PubMed
  5. Ear Nose Throat J. 1993 Apr;72(4):277-9 - PubMed
  6. Br J Neurosurg. 1998 Apr;12(2):165-9 - PubMed
  7. Skeletal Radiol. 1985;13(2):134-46 - PubMed
  8. Bangladesh Med Res Counc Bull. 1990 Jun;16(1):42-5 - PubMed
  9. Head Neck. 2003 Feb;25(2):168-72 - PubMed
  10. Rhinology. 2005 Sep;43(3):225-8 - PubMed
  11. Magn Reson Imaging Clin N Am. 2002 Aug;10(3):467-93 - PubMed
  12. J Laryngol Otol. 1990 Jul;104(7):570-3 - PubMed
  13. Dentomaxillofac Radiol. 2003 Sep;32(5):343-6 - PubMed
  14. Sarcoma. 1999;3(1):11-5 - PubMed
  15. J Comput Assist Tomogr. 1988 Jan-Feb;12(1):143-6 - PubMed
  16. Ann Otolaryngol Chir Cervicofac. 2002 Dec;119(6):363-8 - PubMed
  17. J Laryngol Otol. 2001 Jan;115(1):74-6 - PubMed
  18. Otolaryngol Head Neck Surg. 2001 Dec;125(6):665-7 - PubMed
  19. Neurochirurgie. 2002 Feb;48(1):25-9 - PubMed

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