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Case Rep Nephrol Urol. 2012 Jul;2(2):87-91. doi: 10.1159/000341191. Epub 2012 Jul 10.

Low-grade fibromyxoid sarcoma of the renal pelvis: first report.

Case reports in nephrology and urology

Aristeidis Alevizopoulos, Vasilis Mygdalis, Stayros Tyritzis, K Stravodimos, Constantinos A Constantinides

Affiliations

  1. 1st Academic Urology Department of Athens, Athens University Medical School - LAIKO Hospital, Athens, Greece.

PMID: 23197962 PMCID: PMC3482067 DOI: 10.1159/000341191

Abstract

Sarcomas of the genitourinary tract are quite rare, accounting for 2.1% of all soft tissue sarcomas and have a poor prognosis. Kidney sarcomas are quite rare, representing 1-3% of malignant renal cases. Low-grade fibromyxoid sarcoma (LGFS) of the kidney is an exceedingly uncommon, indolent but metastasizing soft tissue sarcoma with deceptively benign-appearing histological features. The estimated 5-year overall survival seems to be over 90%, but very late local relapses and distant metastasis may occur, which underlines the need for a long-term follow-up. We present a case of a 48-year-old male patient with a LGFS located on the renal pelvis. This is probably the first report of LGFS arising from the renal pelvis.

Keywords: Kidney sarcoma; Low-grade fibromyxoid sarcoma of renal pelvis; Renal pelvis sarcoma; Soft tissue sarcoma

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