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World Allergy Organ J. 2012 Dec;5(12):182-99. doi: 10.1097/WOX.0b013e318279affa.

WAO Guideline for the Management of Hereditary Angioedema.

The World Allergy Organization journal

Timothy Craig, Emel Aygören-Pürsün, Konrad Bork, Tom Bowen, Henrik Boysen, Henriette Farkas, Anete Grumach, Constance H Katelaris, Richard Lockey, Hilary Longhurst, William Lumry, Markus Magerl, Immaculada Martinez-Saguer, Bruce Ritchie, Alexander Nast, Ruby Pawankar, Bruce Zuraw, Marcus Maurer

Affiliations

  1. Department of Medicine, Pediatrics and Graduate Studies, Penn State University, Hershey, PA, USA.

PMID: 23282420 PMCID: PMC3651186 DOI: 10.1097/WOX.0b013e318279affa

Abstract

: Hereditary Angioedema (HAE) is a rare disease and for this reason proper diagnosis and appropriate therapy are often unknown or not available for physicians and other health care providers. For this reason we convened a group of specialists that focus upon HAE from around the world to develop not only a consensus on diagnosis and management of HAE, but to also provide evidence based grades, strength of evidence and classification for the consensus. Since both consensus and evidence grading were adhered to the document meets criteria as a guideline. The outcome of the guideline is to improve diagnosis and management of patients with HAE throughout the world and to help initiate uniform care and availability of therapies to all with the diagnosis no matter where the residence of the individual with HAE exists.

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