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J Clin Diagn Res. 2012 Dec;6(10):1783-5. doi: 10.7860/JCDR/2012/4525.2613. Epub 2012 Dec 15.

The budd-Chiari syndrome in a child: a case report and review of the literature.

Journal of clinical and diagnostic research : JCDR

Vatsala Misra, Kachnar Verma, Dharmendra Kumar Singh, Sri Prakash Misra

Affiliations

  1. Professor Departments of Pathology, Moti Lal Nehru Medical College , Allahabad, Uttar Pradesh, India .

PMID: 23373054 PMCID: PMC3552230 DOI: 10.7860/JCDR/2012/4525.2613

Abstract

The Budd-Chiari Syndrome is associated with hepatic venous outflow obstruction. This syndrome is rare in infants and children. As this syndrome is uncommon, especially in the paediatric age group, misdiagnoses and delays in the diagnosis are frequent. A high index of clinical suspicion along with a radiological aid and a histopathological correlation can lead to an early diagnosis and an appropriate management in such cases.This case report highlights the occurrence of this rare condition in the paediatric age group as well as it redefines the salient features of this syndrome.

Keywords: Centrizonal congestion; Fibrosis; Hepatic venous obstruction; Venography

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