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BMJ Case Rep. 2013 Apr 17;2013. doi: 10.1136/bcr-2013-009097.

Pararenal sclerosing PEComa.

BMJ case reports

Ricardo R Leão, Bruno Jorge Pereira, Vânia Grenha, Hugo Coelho

Affiliations

  1. Serviço de Urologia e Transplantação Renal, Centro Hospitalar Universitário de Coimbra, Portugal. [email protected]

PMID: 23598939 PMCID: PMC3645790 DOI: 10.1136/bcr-2013-009097

Abstract

Small renal or pararenal masses and retroperitoneum lesions are extremely difficult to diagnose. Imaging technology is a precious diagnostic tool; however, it places physicians in a difficult position since many lesions are not precisely diagnosed. Clinical and radiological findings can guide suspicion towards the diagnosis; however, in our current practice most diagnoses are based on histological findings. We aim to present a pararenal sclerosing perivascular epithelioid cell tumour (PEComa), a rare entity, whose diagnosis is only possible through invasive approaches and histological analysis. This rare lesion not only is difficult to diagnose but also has an uncertain behaviour, which is of major importance concerning its follow-up and prognosis. This case report is an attempt to add more data that will help establish criteria for diagnosis and follow-up of this rare disease.

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