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J Clin Neonatol. 2012 Jan;1(1):49-51. doi: 10.4103/2249-4847.92234.

Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born.

Journal of clinical neonatology

Said Younous, Youssef Zarrouki, Mustapha Boutbaoucht, Youssef Mouaffak, Kawtar Ennour El Idrissi, Nissrine Aboussair, Mohammed O Saiad

Affiliations

  1. Department of Anesthesia & Critical Care, Mother and Child Hospital, Mohammed VI University Hospital of Marrakech, Morocco.

PMID: 24027688 PMCID: PMC3761994 DOI: 10.4103/2249-4847.92234

Abstract

Prune belly syndrome (PBS) is a rare congenital anomaly of uncertain etiology. Many associations of PBS with other malformations were previously reported, but only few cases of the association with VACTERL have been described. We report a rare case of a Moroccan new born with PBS and complete VACTERL association. The cause of this association is still unknown, but a common etiology is possible, especially when for the two syndromes, a defect in mesodermal differentiation, in early first trimester, has been suggested.

Keywords: Esophageal atresia; Prune belly syndrome; VACTERL association; new born

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