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J Neurol Surg Rep. 2013 Dec;74(2):92-5. doi: 10.1055/s-0033-1348956. Epub 2013 Sep 09.

Transclival pseudomeningocele secondary to ecchordosis physaliphora: case report and literature review.

Journal of neurological surgery reports

Sakshi Kaul, Osaama H Khan, Idara Edem, Shelley Lwu, Robert Willinsky, Allen Vescan, Gelareh Zadeh

Affiliations

  1. Division of Neurosurgery, Toronto Western Hospital, Toronto, Ontario, Canada.

PMID: 24303343 PMCID: PMC3836942 DOI: 10.1055/s-0033-1348956

Abstract

We describe a 52-year-old woman who presented with meningitis secondary to a pseudomeningocele within the sphenoid sinus derived from a bony defect in the clivus. The bony defect was radiologically characteristic of an ecchordosis physaliphora (EP). She underwent surgical repair of the defect and had resolution of her symptoms. This case report will discuss the second case of transclival pseudomeningocele in the English literature and present EP as a cause.

Keywords: clivus defect; ecchordosis physaliphora; meningitis; pseudomeningocele; transsphenoidal endoscopic surgery

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