Display options
Share it on

Proc (Bayl Univ Med Cent). 2014 Apr;27(2):116-7. doi: 10.1080/08998280.2014.11929077.

Celiac artery disease and fatal rupture of a hepatic artery aneurysm in the Ehlers-Danlos syndrome.

Proceedings (Baylor University. Medical Center)

Amritpal Nat, Tanya George, Gregory Mak, Amit Sharma, Amitpal Nat, Robert Lebel

Affiliations

  1. State University of New York Upstate Medical University, Syracuse, New York.

PMID: 24688192 PMCID: PMC3954662 DOI: 10.1080/08998280.2014.11929077

Abstract

Isolated visceral arteriopathies of the celiac and hepatic artery are rare. We present a case of a Caucasian man who presented with abdominal pain and was found to have a spontaneous celiac artery dissection. Genetic analysis revealed a mutation consistent with Ehlers-Danlos syndrome type IV. The patient died 2 months later from a spontaneous rupture of his hepatic artery.

References

  1. Orphanet J Rare Dis. 2007 Jul 19;2:32 - PubMed

Publication Types