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Adv Biomed Res. 2014 Sep 12;3:191. doi: 10.4103/2277-9175.140623. eCollection 2014.

Hallervorden-Spatz disease.

Advanced biomedical research

Maseumeh Dashti, Ahmad Chitsaz

Affiliations

  1. Department of Neurology, Shahid Sadooghi Hospital, Isfahan, Iran.

PMID: 25317409 PMCID: PMC4190451 DOI: 10.4103/2277-9175.140623

Abstract

Hallervorden-Spatz disease (HSD) is a rare disorder characterized by progressive extrapyramidal dysfunction and dementia. Hallervorden and Spatz first described the disease, in 1922 as a form of familial brain degeneration characterized by iron deposition in the brain. Here we present four HSD cases with different clinical pictures.

Keywords: Extra pyramdal sign; Hallervorden-Spatz Disease; dementia; dystonia

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