Display options
Cite
Ganczar J, English R. Uhl's anomaly: Absence of the right ventricular myocardium. Ann Pediatr Cardiol. 2015;8(1):71-3doi: 10.4103/0974-2069.149529.
Ganczar, J., & English, R. (2015). Uhl's anomaly: Absence of the right ventricular myocardium. Annals of pediatric cardiology, 8(1), 71-3. https://doi.org/10.4103/0974-2069.149529
Ganczar, Joanna, and English, Robert. "Uhl's anomaly: Absence of the right ventricular myocardium." Annals of pediatric cardiology vol. 8,1 (2015): 71-3. doi: https://doi.org/10.4103/0974-2069.149529
Ganczar J, English R. Uhl's anomaly: Absence of the right ventricular myocardium. Ann Pediatr Cardiol. 2015 Jan-Apr;8(1):71-3. doi: 10.4103/0974-2069.149529. PMID: 25684894; PMCID: PMC4322408.
Copy Download .nbib Format: NLM
Share it on

Ann Pediatr Cardiol. 2015 Jan-Apr;8(1):71-3. doi: 10.4103/0974-2069.149529.

Uhl's anomaly: Absence of the right ventricular myocardium.

Annals of pediatric cardiology

Joanna Ganczar, Robert English

Affiliations

  1. Department of Pediatrics, College of Medicine, University of Florida, Jacksonville, Florida, USA.
  2. Department of Pediatric Cardiology, College of Medicine, University of Florida, Jacksonville, Florida, USA.

PMID: 25684894 PMCID: PMC4322408 DOI: 10.4103/0974-2069.149529

Abstract

We report a case of Uhl's anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was established with a myocardial biopsy.

Keywords: Cyanosis in an infant; Uhl’sanomaly; right ventricular dysfunction; right-sided heart failure

References

  1. Indian J Med Res. 2010 Jan;131:35-45 - PubMed
  2. Cardiol Young. 2002 Mar;12(2):192-5 - PubMed
  3. Bull Johns Hopkins Hosp. 1952 Sep;91(3):197-209 - PubMed
  4. Arq Bras Cardiol. 2001 Jul;77(1):69-76 - PubMed
  5. Asian Cardiovasc Thorac Ann. 2009 Apr;17(2):203-5 - PubMed
  6. Circulation. 1996 Apr 15;93(8):1588-600 - PubMed
  7. Br Heart J. 1993 Feb;69(2):142-50 - PubMed
  8. Circulation. 1996 Apr 15;93(8):1483-4 - PubMed
  9. Int J Cardiol. 2012 Jan 26;154(2):e36-7 - PubMed

Publication Types