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Schottlaender LV, Correale J, Ameriso SF, et al. White matter relapsing remitting disease: "Susac's syndrome"-An underdiagnosed entity. Mult Scler Relat Disord. 2013;2(4):349-54doi: 10.1016/j.msard.2013.02.007.
Schottlaender, L. V., Correale, J., Ameriso, S. F., Moschini, J. A., Crivelli, L., Meli, F., & Fiol, M. P. (2013). White matter relapsing remitting disease: "Susac's syndrome"-An underdiagnosed entity. Multiple sclerosis and related disorders, 2(4), 349-54. https://doi.org/10.1016/j.msard.2013.02.007
Schottlaender, Lucia V, et al. "White matter relapsing remitting disease: "Susac's syndrome"-An underdiagnosed entity." Multiple sclerosis and related disorders vol. 2,4 (2013): 349-54. doi: https://doi.org/10.1016/j.msard.2013.02.007
Schottlaender LV, Correale J, Ameriso SF, Moschini JA, Crivelli L, Meli F, Fiol MP. White matter relapsing remitting disease: "Susac's syndrome"-An underdiagnosed entity. Mult Scler Relat Disord. 2013 Oct;2(4):349-54. doi: 10.1016/j.msard.2013.02.007. Epub 2013 Apr 09. PMID: 25877845.
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Mult Scler Relat Disord. 2013 Oct;2(4):349-54. doi: 10.1016/j.msard.2013.02.007. Epub 2013 Apr 09.

White matter relapsing remitting disease: "Susac's syndrome"-An underdiagnosed entity.

Multiple sclerosis and related disorders

Lucia V Schottlaender, Jorge Correale, Sebastian F Ameriso, Javier A Moschini, Lucia Crivelli, Francisco Meli, Marcela P Fiol

Affiliations

  1. Department of Neurology, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].
  2. Department of Neurology, Neuroimmunology Section, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].
  3. Department of Neurology, Vascular Neurology Section, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].
  4. Department of Neurology, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].
  5. Department of Neurology, Neuroimmunology Section, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].
  6. Department of Neurology, Neuroimaging Section, Institute for Neurological Research (FLENI) Dr Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].
  7. Department of Neurology, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: [email protected].

PMID: 25877845 DOI: 10.1016/j.msard.2013.02.007

Abstract

Susac's syndrome is a treatable microangiopathy of unknown etiology affecting arterioles of the brain, retina, and cochlea. The typical clinical manifestation is the triad of encephalopathy, visual loss, and sensorineural hearing loss. One or more of these features may not be present at onset and therefore Susac's syndrome's diagnosis may be difficult. We describe the clinical presentation, diagnostic tests, and treatment of three cases diagnosed and treated at our institution.

Copyright © 2013 Elsevier B.V. All rights reserved.

Keywords: Cochlea; Corpus callosum; Encephalopathy; Retina; Susac's syndrome; White matter disease

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