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Indian J Anaesth. 2015 May;59(5):312-4. doi: 10.4103/0019-5049.156888.

Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management.

Indian journal of anaesthesia

Anshuman Singh, V K Pandey, Manish Tandon, C K Pandey

Affiliations

  1. Department of Anesthesia and Critical Care, Institute of Liver and Biliary Sciences, New Delhi, India.

PMID: 26019357 PMCID: PMC4445154 DOI: 10.4103/0019-5049.156888

Abstract

Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation.

Keywords: Cirrhosis; dyskeratosis congenita; liver transplant; transplant

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