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J Neonatal Surg. 2013 Apr 01;2(2):21. eCollection 2013.

Esophageal atresia and tracheoesophageal fistula with unilateral pulmonary agenesis - hypoplasia.

Journal of neonatal surgery

Shraddha Verma, Jai Kumar Mahajan, Katragadda Laxmi Narsimha Rao

Affiliations

  1. Department of Pediatric Surgery, PGIMER, Chandigarh, India.

PMID: 26023441 PMCID: PMC4420375

Abstract

Association of unilateral severe pulmonary hypoplasia or agenesis and esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) is an exceedingly rare and highly lethal combination. We report a case of full term male baby who had EA with TEF and right lung hypoplasia, managed at our centre. He is alive and doing well at 10 years of age.

Keywords: Esophageal atresia; Pulmonary agenesis; Tracheoesophageal fistula

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