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Respir Med Case Rep. 2015 Jun 04;16:38-40. doi: 10.1016/j.rmcr.2015.05.016. eCollection 2015.

An unusual presentation of pulmonary epitheloid hemangioendothelioma.

Respiratory medicine case reports

Jaya Prakash Sugunaraj, Claire Pedroso, Shravan Kethireddy, Mohammed Mogri

Affiliations

  1. Geisinger Medical Center, USA.

PMID: 26744650 PMCID: PMC4681899 DOI: 10.1016/j.rmcr.2015.05.016

Abstract

Pulmonary epitheloid hemangioendothelioma (PEHE) is a rare, often incidentally diagnosed, endothelial tumor of the lung. We present a case of a young adult who presented with acute hypoxemic respiratory failure and severe pulmonary hypertension with subsequent imaging and tissue biopsy confirming a diagnosis of PEHE. We briefly highlight the unique clinical, radiographic and histopathologic aspects of this rare disease. We propose that PEHE should be considered in the differential diagnosis for acute hypoxemic respiratory failure associated with bilateral pulmonary cavitary nodules and bronchoscopy should be considered as an initial diagnostic test.

Keywords: Broncoscopy; Cavitary nodules; Pulmonary epitheloid hemangioendothelioma (PEHE)

References

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