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J Indian Assoc Pediatr Surg. 2015 Oct-Dec;20(4):194-6. doi: 10.4103/0971-9261.154671.

Kaposiform hemangioendothelioma with Kasabach-Merritt phenomenon in a neonate of life- and limb-threatening nature: A case report.

Journal of Indian Association of Pediatric Surgeons

Anoop Subash, Ganesh K Senthil, Ramkumar Ramamoorthy, Andal Appasamy, Namasivayam Selvarajan

Affiliations

  1. Department of Paediatric Surgery, Kanchi Kamakoti Childs Trust Hospital, Nungambakkam, Chennai, Tamil Nadu, India.
  2. Department of Dermatology, Kanchi Kamakoti Childs Trust Hospital, Nungambakkam, Chennai, Tamil Nadu, India.
  3. Department of Paediatrics, Kanchi Kamakoti Childs Trust Hospital, Nungambakkam, Chennai, Tamil Nadu, India.

PMID: 26628813 PMCID: PMC4586984 DOI: 10.4103/0971-9261.154671

Abstract

Kaposiform hemangioendothelioma involving whole of a leg in a neonate with Kasabach-Merritt phenomenon causing limb and life-threatening situation has not been reported. One such case and its successful management is presented in this case report. Literature review is made.

Keywords: Infant-Newborn; Kaposiform hemangioendothelioma; Kasabach-merritt phenomenon; vincristine

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