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J Ophthalmic Vis Res. 2015 Jul-Sep;10(3):320-8. doi: 10.4103/2008-322X.170353.

Circumscribed Choroidal Hemangioma.

Journal of ophthalmic & vision research

Saeed Karimi, Ramin Nourinia, Arman Mashayekhi

Affiliations

  1. Ophthalmic Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
  2. Ocular Oncology Service, Wills Eye Institute, Thomas Jefferson University, Philadelphia, PA, USA.

PMID: 26730320 PMCID: PMC4687268 DOI: 10.4103/2008-322X.170353

Abstract

Circumscribed choroidal hemangiomas are benign vascular hamartomas without systemic associations. Generally, they are orange-red elevated masses, which are found posterior to the equator. Lesions are usually solitary and unilateral. Overlying subretinal fluid, serous retinal detachment and cystoid macular edema are common findings. Intravenous fluorescein angiography, indocyanine green angiography, ultrasonography, optical coherence tomography and enhanced depth imaging are helpful ancillary tests for diagnosis of circumscribed choroidal hemangiomas. Asymptomatic circumscribed choroidal hemangiomas do not require treatment. For symptomatic lesions with exudative retinal detachment or cystoid macular edema, photodynamic therapy has emerged as the treatment of choice with high rates of tumor regression, subretinal fluid resorption and minimal complications. Lens-sparing external beam radiotherapy, plaque brachytherapy, proton beam therapy, stereotactic radiosurgery, transpupillary thermotherapy, laser photocoagulation and anti-VEGF injections are other treatment modalities.

Keywords: Circumscribed Choroidal Hemangioma; Photodynamic Therapy; Subretinal Fluid

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