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Pulm Circ. 2016 Mar;6(1):118-25. doi: 10.1086/685102.

Cardiac catheterization in children with pulmonary hypertensive vascular disease: consensus statement from the Pulmonary Vascular Research Institute, Pediatric and Congenital Heart Disease Task Forces.

Pulmonary circulation

Maria Jesus Del Cerro, Shahin Moledina, Sheila G Haworth, Dunbar Ivy, Maha Al Dabbagh, Hanaa Banjar, Gabriel Diaz, Alexandria Heath-Freudenthal, Ahmed Nasser Galal, Tilman Humpl, Snehal Kulkarni, Antonio Lopes, Ana Olga Mocumbi, G D Puri, Beyra Rossouw, S Harikrishnan, Anita Saxena, Patience Udo, Lina Caicedo, Omar Tamimi, Ian Adatia

Affiliations

  1. Ramón y Cajal University Hospital, Madrid, Spain.
  2. Great Ormond Street Hospital, London, United Kingdom.
  3. University College London, London, United Kingdom.
  4. Children's Hospital Colorado, Aurora, Colorado, USA.
  5. King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia.
  6. King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia.
  7. Universidad Nacional de Colombia, Bogota, Colombia.
  8. Kardiozentrum, La Paz, Bolivia.
  9. University of Toronto and Hospital for Sick Children, Toronto, Ontario, Canada.
  10. Kokilaben Dhirubai Ambani Hospital and Medical Research Institute, Mumbai, India.
  11. University of São Paulo, São Paulo, Brazil.
  12. National Institute of Health, Maputo, Mozambique.
  13. Postgraduate Institute of Medical Education and Research, Chandigarh, India.
  14. University of Cape Town, Cape Town, South Africa.
  15. Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
  16. All-India Institute of Medical Sciences, New Delhi, India.
  17. University of Uyo Hospital, Uyo, Nigeria.
  18. Clinica Shaio, Bogota, Colombia.
  19. King Saud bin Abdulaziz University, Riyadh, Saudi Arabia.
  20. Stollery Children's Hospital, Edmonton, Alberta, Canada; on behalf of the PVRI Pediatric Task Force members Steven Abman, Vera Aiello, Rolf Berger, Patricia Cortez, Jeffrey Fineman, Marilyne Lévy, Marlene Rabinovitch, J. Usha Raj, Irwin Reiss, Julio Sandoval, Kurt Stenmark, and Rao Sureshi.

PMID: 27076908 PMCID: PMC4809667 DOI: 10.1086/685102

Abstract

Cardiac catheterization is important in the diagnosis and risk stratification of pulmonary hypertensive vascular disease (PHVD) in children. Acute vasoreactivity testing provides key information about management, prognosis, therapeutic strategies, and efficacy. Data obtained at cardiac catheterization continue to play an important role in determining the surgical options for children with congenital heart disease and clinical evidence of increased pulmonary vascular resistance. The Pediatric and Congenital Heart Disease Task Forces of the Pulmonary Vascular Research Institute met to develop a consensus statement regarding indications for, conduct of, acute vasoreactivity testing with, and pitfalls and risks of cardiac catheterization in children with PHVD. This document contains the essentials of those discussions to provide a rationale for the hemodynamic assessment by cardiac catheterization of children with PHVD.

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