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Case Rep Endocrinol. 2016;2016:6785925. doi: 10.1155/2016/6785925. Epub 2016 Jun 16.

Plurihormonal Cosecretion by a Case of Adrenocortical Oncocytic Neoplasm.

Case reports in endocrinology

J J Corrales, C Robles-Lázaro, A I Sánchez-Marcos, M C González-Sánchez, P Antúnez-Plaza, J M Miralles

Affiliations

  1. Servicio de Endocrinología y Nutrición, Hospital Clínico Universitario, Paseo de San Vicente No. 58, 37007 Salamanca, Spain; Departamento de Medicina, Universidad de Salamanca, Campus Miguel de Unamuno s/n, 37007 Salamanca, Spain; Centro de Investigación del Cáncer (IBMCC-CSIC/USAL) and Instituto Biosanitario de Salamanca, Campus Miguel de Unamuno s/n, 37007 Salamanca, Spain.
  2. Servicio de Endocrinología y Nutrición, Hospital Clínico Universitario, Paseo de San Vicente No. 58, 37007 Salamanca, Spain.
  3. Servicio de Endocrinología y Nutrición, Hospital Clínico Universitario, Paseo de San Vicente No. 58, 37007 Salamanca, Spain; Departamento de Medicina, Universidad de Salamanca, Campus Miguel de Unamuno s/n, 37007 Salamanca, Spain.
  4. Unidad de Cirugía Endocrina, Departamento de Cirugía, Hospital Clínico Universitario de Salamanca, Paseo de San Vicente No. 58, 37007 Salamanca, Spain.
  5. Servicio de Anatomía Patológica, Departamento de Anatomía Patológica, Hospital Universitario de Salamanca, Paseo de San Vicente No. 58, 37007 Salamanca, Spain.

PMID: 27413559 PMCID: PMC4927977 DOI: 10.1155/2016/6785925

Abstract

Adrenocortical oncocytic neoplasms (oncocytomas) are extremely rare; only approximately 159 cases have been described so far. The majority are nonfunctional and benign. We describe an unusual case of a functional oncocytoma secreting an excess of glucocorticoids (cortisol) and androgens (androstenedione and DHEAS), a pattern of plurihormonal cosecretion previously not reported in men, presenting with endocrine manifestations of Cushing's syndrome. The neoplasm was considered to be of uncertain malignant potential (borderline) according to the Lin-Weiss-Bisceglia criteria.

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