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Deemer KS, Alvarez GF. A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome. Case Rep Crit Care. 2016;2016:6072909doi: 10.1155/2016/6072909.
Deemer, K. S., & Alvarez, G. F. (2016). A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome. Case reports in critical care, 20166072909. https://doi.org/10.1155/2016/6072909
Deemer, Kirsten S, and Alvarez, George F. "A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome." Case reports in critical care vol. 2016 (2016): 6072909. doi: https://doi.org/10.1155/2016/6072909
Deemer KS, Alvarez GF. A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome. Case Rep Crit Care. 2016;2016:6072909. doi: 10.1155/2016/6072909. Epub 2016 Jul 25. PMID: 27699071; PMCID: PMC5035668.
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Case Rep Crit Care. 2016;2016:6072909. doi: 10.1155/2016/6072909. Epub 2016 Jul 25.

A Rare Case of Persistent Lactic Acidosis in the ICU: Glycogenic Hepatopathy and Mauriac Syndrome.

Case reports in critical care

Kirsten S Deemer, George F Alvarez

Affiliations

  1. Department of Critical Care Medicine, South Health Campus ICU, 4448 Front Street SE, Calgary, AB, Canada T3M 1M4.
  2. Department of Critical Care Medicine, University of Calgary, AB, Canada.

PMID: 27699071 PMCID: PMC5035668 DOI: 10.1155/2016/6072909

Abstract

Mauriac syndrome is a rare disorder that can present with the single feature of glycogenic hepatopathy in children and adults with poorly controlled diabetes mellitus. An often underrecognized finding of glycogenic hepatopathy is lactic acidosis and hyperlactatemia. Primary treatment of glycogenic hepatopathy is improved long-term blood glucose control. Resolution of symptoms and hepatomegaly will occur with improvement in hemoglobin A1C. We present here a case of a young adult female presenting to the intensive care unit with Mauriac syndrome. This case demonstrates

References

  1. JAMA. 2015 Feb 24;313(8):849-50 - PubMed
  2. Diabetes Care. 2015 Feb;38(2):e11-2 - PubMed
  3. Case Rep Gastroenterol. 2015 Jul 09;9(2):221-6 - PubMed
  4. Arch Dis Child. 2014 Apr;99(4):354-7 - PubMed
  5. Ann Hepatol. 2012 Jul-Aug;11(4):554-8 - PubMed
  6. Scand J Clin Lab Invest. 2013;73(4):293-9 - PubMed
  7. Cleve Clin J Med. 2015 Sep;82(9):615-24 - PubMed
  8. N Engl J Med. 2014 Dec 11;371(24):2309-19 - PubMed
  9. World J Diabetes. 2014 Dec 15;5(6):882-8 - PubMed
  10. Am J Surg Pathol. 2006 Apr;30(4):508-13 - PubMed

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