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Molinaro F, Garzi A, Cerchia E, et al. Sternal reconstruction by extracellular matrix: a rare case of phaces syndrome. Open Med (Wars). 2016;11(1):196-199doi: 10.1515/med-2016-0037.
Molinaro, F., Garzi, A., Cerchia, E., Di Crescenzo, V. G., Luzzi, L., Bulotta, A. L., Gotti, G., & Messina, M. (2016). Sternal reconstruction by extracellular matrix: a rare case of phaces syndrome. Open medicine (Warsaw, Poland), 11(1), 196-199. https://doi.org/10.1515/med-2016-0037
Molinaro, Francesco, et al. "Sternal reconstruction by extracellular matrix: a rare case of phaces syndrome." Open medicine (Warsaw, Poland) vol. 11,1 (2016): 196-199. doi: https://doi.org/10.1515/med-2016-0037
Molinaro F, Garzi A, Cerchia E, Di Crescenzo VG, Luzzi L, Bulotta AL, Gotti G, Messina M. Sternal reconstruction by extracellular matrix: a rare case of phaces syndrome. Open Med (Wars). 2016 Jun 23;11(1):196-199. doi: 10.1515/med-2016-0037. eCollection 2016. PMID: 28352793; PMCID: PMC5329824.
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Open Med (Wars). 2016 Jun 23;11(1):196-199. doi: 10.1515/med-2016-0037. eCollection 2016.

Sternal reconstruction by extracellular matrix: a rare case of phaces syndrome.

Open medicine (Warsaw, Poland)

Francesco Molinaro, Alfredo Garzi, Elisa Cerchia, Vincenzo Giuseppe Di Crescenzo, Luca Luzzi, Anna Lavinia Bulotta, Giuseppe Gotti, Mario Messina

Affiliations

  1. Division of Pediatric Surgery, Department of Medical, Surgical and Neurological Sciences, University of Siena, Italy.
  2. University Salerno, Salerno, Italy.
  3. Department of Medical, Surgical and Neurological Science. Pediatric Surgery Unit, University of Siena, Italy.
  4. Department of Medicine and Surgery, Thoracic Surgery Unit, University of Salerno, Italy.
  5. Thoracic Surgery Unit, University Hospital of Siena, Siena, Italy.

PMID: 28352793 PMCID: PMC5329824 DOI: 10.1515/med-2016-0037

Abstract

Congenital defects of the sternum are rare and due to a failure of midline development and fusion of the sternal bones. Surgical correction of a sternal cleft should be preferred during infancy for functional reasons. Chest wall reconstruction represented a complex problem in the last decades. We report our successful outcome of sternal reconstruction in a rare case of PHACES syndrome, in which the patient was submitted to reconstruction of the sternum and complete closure of the thoracic defect by the employ of an extracellular matrix XCM Biologic tissue matrix. We promote the use of extracellular matrix in surgical reconstruction of chest defects for its maneuverability, plasticity, tolerability and the possibility of growing with the children's chest getting a good compliance and optimal cosmetic results.

Keywords: Midline development defects; Phaces syndrome; Sternal reconstruction

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