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Ghosh R, Shetty V, Hegde S, et al. Rare features associated with Mobius syndrome: Report of two cases. J Dent Res Dent Clin Dent Prospects. 2017;11(1):60-65doi: 10.15171/joddd.2017.012.
Ghosh, R., Shetty, V., Hegde, S., Babu, G. S., Ajila, V., Kishore P, N., & Nair, M. (2017). Rare features associated with Mobius syndrome: Report of two cases. Journal of dental research, dental clinics, dental prospects, 11(1), 60-65. https://doi.org/10.15171/joddd.2017.012
Ghosh, Rumela, et al. "Rare features associated with Mobius syndrome: Report of two cases." Journal of dental research, dental clinics, dental prospects vol. 11,1 (2017): 60-65. doi: https://doi.org/10.15171/joddd.2017.012
Ghosh R, Shetty V, Hegde S, Babu GS, Ajila V, Kishore P N, Nair M. Rare features associated with Mobius syndrome: Report of two cases. J Dent Res Dent Clin Dent Prospects. 2017;11(1):60-65. doi: 10.15171/joddd.2017.012. Epub 2017 Mar 15. PMID: 28413599; PMCID: PMC5390129.
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J Dent Res Dent Clin Dent Prospects. 2017;11(1):60-65. doi: 10.15171/joddd.2017.012. Epub 2017 Mar 15.

Rare features associated with Mobius syndrome: Report of two cases.

Journal of dental research, dental clinics, dental prospects

Rumela Ghosh, Vikram Shetty, Shruthi Hegde, G Subhas Babu, Vidya Ajila, Nanda Kishore P, Mithula Nair

Affiliations

  1. Department of Oral Medicine and Radiology, A B Shetty Memorial Institute of Dental Sciences, Nitte University, Mangalore, India.
  2. Nitte Meenakshi Institute of Craniofacial Surgery, K.S.Hegde Medical College and Hospital, Nitte University, Mangalore, India.
  3. Department of Orthodontics, A B Shetty Memorial Institute of Dental Sciences, Nitte University, Mangalore, India.

PMID: 28413599 PMCID: PMC5390129 DOI: 10.15171/joddd.2017.012

Abstract

Mobius syndrome is a rare congenital disorder with the preliminary diagnostic criteria of congenital facial and abducent nerve palsy. Involvement of other cranial nerves, too, is common. Prevalence rate of this syndrome is approximately 1 in 100,000 neonates. It is of unknown etiology with sporadic occurrence. However, data regarding the occurrence rate in India is limited. Features such as orofacial malformations, limb defects, and musculoskeletal, behavioral, and cognitive abnormalities might be associated. A thorough evaluation to identify the condition and establishing an adequate treatment plan is of utmost important in this condition. We are reporting clinical and radiographic features of Mobius syndrome in two cases along with unusual findings of limb and neck deformity.

Keywords: Congenital; facial nerve; mobius syndrome; palsy; strabismus

References

  1. J Craniomaxillofac Surg. 2013 Jan;41(1):e1-4 - PubMed
  2. Ital J Pediatr. 2016 Jun 03;42(1):56 - PubMed
  3. Plast Reconstr Surg. 1998 Sep;102(4):961-7 - PubMed
  4. Brain. 2005 Jul;128(Pt 7):1728-36 - PubMed
  5. MCN Am J Matern Child Nurs. 2008 Sep-Oct;33(5):272-8; quiz 279-80 - PubMed
  6. Int J Paediatr Dent. 2002 Nov;12(6):446-9 - PubMed
  7. Neurology. 2000 Oct 10;55(7):1058-60 - PubMed
  8. ASDC J Dent Child. 1997 Jan-Feb;64(1):64-7 - PubMed
  9. J Med Genet. 1990 Feb;27(2):122-6 - PubMed
  10. Clin Plast Surg. 2002 Oct;29(4):497-514 - PubMed

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