Display options
Cite
Fei N, Sofka S. Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera. Case Rep Hematol. 2017;2017:9091612doi: 10.1155/2017/9091612.
Fei, N., & Sofka, S. (2017). Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera. Case reports in hematology, 20179091612. https://doi.org/10.1155/2017/9091612
Fei, Naomi, and Sofka, Sarah. "Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera." Case reports in hematology vol. 2017 (2017): 9091612. doi: https://doi.org/10.1155/2017/9091612
Fei N, Sofka S. Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera. Case Rep Hematol. 2017;2017:9091612. doi: 10.1155/2017/9091612. Epub 2017 Jun 04. PMID: 28660085; PMCID: PMC5474248.
Copy Download .nbib Format: NLM
Share it on

Case Rep Hematol. 2017;2017:9091612. doi: 10.1155/2017/9091612. Epub 2017 Jun 04.

Dermatomyositis Associated with Myelofibrosis following Polycythemia Vera.

Case reports in hematology

Naomi Fei, Sarah Sofka

Affiliations

  1. Department of Internal Medicine, West Virginia University Hospital, 1 Medical Center Dr., Morgantown, WV 26505, USA.

PMID: 28660085 PMCID: PMC5474248 DOI: 10.1155/2017/9091612

Abstract

Dermatomyositis (DM) is a unique inflammatory myopathy with clinical findings of proximal muscle weakness, characteristic rash, and elevated muscle enzymes. The association of DM and malignancy, most commonly adenocarcinoma, is well known. There have been few case reports of primary myelofibrosis associated with DM. We present the case of a 69-year-old male with a history of polycythemia vera (PV) who developed proximal muscle weakness, dysphagia, and rash. He was found to have elevated creatinine kinase and skin biopsy was consistent with DM. Due to persistent pancytopenia a bone marrow biopsy was performed and showed postpolycythemic myelofibrosis. To our knowledge, this is the first case reported of this unique association.

References

  1. Ann Hematol. 2008 Dec;87(12):1019-20 - PubMed
  2. Arch Dermatol. 1980 Mar;116(3):295-8 - PubMed
  3. N Engl J Med. 1992 Feb 6;326(6):363-7 - PubMed
  4. Am J Hematol. 2003 Nov;74(3):175-8 - PubMed
  5. Actas Dermosifiliogr. 2014 Nov;105(9):876-8 - PubMed
  6. Int J Hematol. 1997 Oct;66(3):345-51 - PubMed
  7. PLoS One. 2011 Apr 18;6(4):e18522 - PubMed
  8. J Clin Aesthet Dermatol. 2017 Jan;10 (1):57-62 - PubMed
  9. Am J Hematol. 2006 Jul;81(7):559-60 - PubMed
  10. Case Rep Urol. 2016;2016:7050981 - PubMed
  11. J Exp Med. 2005 Feb 21;201(4):591-601 - PubMed
  12. Lancet. 2001 Jan 13;357(9250):96-100 - PubMed
  13. Autoimmun Rev. 2012 Jul;11(9):615-20 - PubMed
  14. Case Rep Gastroenterol. 2016 Jun 27;10(2):338-43 - PubMed
  15. Leuk Lymphoma. 2003 Mar;44(3):539-41 - PubMed
  16. Australas J Dermatol. 2012 Aug;53(3):e58-60 - PubMed
  17. Rinsho Shinkeigaku. 2006 Mar;46(3):210-3 - PubMed
  18. Clin Rheumatol. 2007 Jul;26(7):1198-200 - PubMed
  19. N Engl J Med. 2014 Dec 25;371(26):2537-8 - PubMed
  20. Ann Intern Med. 1976 Jan;84(1):68-76 - PubMed
  21. BMJ Case Rep. 2016 Jul 08;2016: - PubMed
  22. Ann Rheum Dis. 1991 Mar;50(3):191-5 - PubMed
  23. Leuk Lymphoma. 1997 Feb;24(5-6):483-9 - PubMed
  24. Br J Dermatol. 2013 Oct;169(4):838-47 - PubMed
  25. Hematology. 2001;6(2):131-4 - PubMed
  26. JAMA. 2004 May 19;291(19):2367-75 - PubMed
  27. Dermatology. 2001;202(2):123-6 - PubMed
  28. Biochem Pharmacol. 2012 May 1;83(9):1136-45 - PubMed

Publication Types

Grant support