Display options
Share it on

J Arrhythm. 2017 Jun;33(3):237-239. doi: 10.1016/j.joa.2016.10.561. Epub 2016 Nov 10.

Epicardially placed implantable cardioverter-defibrillator for a child with congenital long QT syndrome.

Journal of arrhythmia

Hirotaro Sugiyama, Motomi Tachibana, Hiroshi Morita, Nobuhiro Nishii, Akihito Miyoshi, Hiroyasu Sugiyama, Koji Nakagawa, Atsuyuki Watanabe, Kazufumi Nakamura, Hiroshi Ito

Affiliations

  1. Department of Cardiology, Okayama University Hospital, 2-5-1 Shikata-cho, Kita-ku, Okayama 700-8558, Japan.

PMID: 28607621 PMCID: PMC5459415 DOI: 10.1016/j.joa.2016.10.561

Abstract

A 7-year-old boy presented at our hospital with syncope. At birth, electrocardiography had shown a long QT interval with torsade de pointes (TdP). Congenital long QT syndrome (LQTS) had been diagnosed by genetic testing, and was successfully controlled with oral propranolol. At age 7, TdP had recurred with syncope. Electrocardiography revealed a prominent long QT interval with T-wave alternans. The propranolol dose was increased, but TdP remained uncontrolled. A cardioverter-defibrillator (ICD) was implanted epicardially, and TdP completely resolved with atrial pacing. We report this rare case of ICD implantation in a child with LQTS.

Keywords: Congenital long QT syndrome; ICD, implantable cardioverter-defibrillator; Implantable cardioverter-defibrillator; LQTS, long QT syndrome; TdP, torsade de pointes

References

  1. J Am Coll Cardiol. 2009 Aug 25;54(9):832-7 - PubMed
  2. Heart Rhythm. 2010;7(2):193-8 - PubMed
  3. Tex Heart Inst J. 2011;38(4):421-3 - PubMed
  4. Surg Today. 2014 Oct;44(10):1801-6 - PubMed

Publication Types