Display options
Cite
Seedat F, Kalla IS, Feldman C. Unilateral absent pulmonary artery in an adult - A diagnostic and therapeutic challenge. Respir Med Case Rep. 2017;22:238-242doi: 10.1016/j.rmcr.2017.09.004.
Seedat, F., Kalla, I. S., & Feldman, C. (2017). Unilateral absent pulmonary artery in an adult - A diagnostic and therapeutic challenge. Respiratory medicine case reports, 22238-242. https://doi.org/10.1016/j.rmcr.2017.09.004
Seedat, Faheem, et al. "Unilateral absent pulmonary artery in an adult - A diagnostic and therapeutic challenge." Respiratory medicine case reports vol. 22 (2017): 238-242. doi: https://doi.org/10.1016/j.rmcr.2017.09.004
Seedat F, Kalla IS, Feldman C. Unilateral absent pulmonary artery in an adult - A diagnostic and therapeutic challenge. Respir Med Case Rep. 2017 Sep 14;22:238-242. doi: 10.1016/j.rmcr.2017.09.004. eCollection 2017. PMID: 28951831; PMCID: PMC5604951.
Copy Download .nbib Format: NLM
Share it on

Respir Med Case Rep. 2017 Sep 14;22:238-242. doi: 10.1016/j.rmcr.2017.09.004. eCollection 2017.

Unilateral absent pulmonary artery in an adult - A diagnostic and therapeutic challenge.

Respiratory medicine case reports

Faheem Seedat, Ismail S Kalla, Charles Feldman

Affiliations

  1. Department of Internal Medicine, Faculty of Health Sciences, University of Witwatersrand, Johannesburg, South Africa.
  2. Division of Pulmonology, Department of Internal Medicine, Charlotte Maxeke Johannesburg Academic Hospital and Faculty of Health Sciences, University of Witwatersrand, Johannesburg, South Africa.

PMID: 28951831 PMCID: PMC5604951 DOI: 10.1016/j.rmcr.2017.09.004

Abstract

Unilateral absent pulmonary artery (UAPA) is a congenital abnormality rarely diagnosed in adults. UAPA has a myriad of clinical presentations and pulmonary hypertension is present in a quarter of all cases. Isolated UAPA commonly affects the right pulmonary artery and occurs as a result of abnormal development of the sixth aortic arch segment. Due to its rarity, it remains a diagnostic and therapeutic challenge. We describe a case of UAPA in an adult presenting with severe pulmonary hypertension. We describe the appropriate diagnostic approach to a patient with pulmonary hypertension and illustrate the importance of a detailed evaluation to determine the underlying aetiology, particularly in rare causes. Furthermore, we review the clinical presentation, diagnosis and management challenges of UAPA in adults.

Keywords: CTEPH, Chronic thromboembolic pulmonary hypertension; CTPA, Computed tomography pulmonary angiogram; Diagnosis; ECG, Electrocardiogram; MRI, Magnetic resonance imaging; Pulmonary hypertension; SVT, Supraventricular tachycardia; Therapy; UAPA, Unilateral absent pulmonary artery; Unilateral absent pulmonary artery

References

  1. J Radiol Case Rep. 2010;4(11):32-7 - PubMed
  2. Interact Cardiovasc Thorac Surg. 2008 Dec;7(6):1183-5 - PubMed
  3. Eur J Cardiothorac Surg. 2004 Sep;26(3):508-14 - PubMed
  4. Chest. 1995 Sep;108(3):670-6 - PubMed
  5. J Thorac Cardiovasc Surg. 2011 Jan;141(1):171-8 - PubMed
  6. AJR Am J Roentgenol. 2013 Feb;200(2):W101-15 - PubMed
  7. Clin Radiol. 2007 Mar;62(3):238-44 - PubMed
  8. Hippokratia. 2013 Jan;17(1):73-6 - PubMed
  9. AJR Am J Roentgenol. 2002 Nov;179(5):1253-60 - PubMed
  10. J Thorac Cardiovasc Surg. 2011 Jan;141(1):7-15 - PubMed
  11. Chest. 2009 Aug;136(2):628-632 - PubMed
  12. Proc (Bayl Univ Med Cent). 2012 Apr;25(2):115-8 - PubMed
  13. Lung India. 2009 Jan;26(1):26-9 - PubMed
  14. Arch Cardiovasc Dis. 2013 Aug-Sep;106(8-9):448-54 - PubMed
  15. Circulation. 2010 Jun 15;121(23 ):e434-6 - PubMed
  16. Semin Thorac Cardiovasc Surg. 2011 Autumn;23(3):196-202 - PubMed
  17. Circulation. 2009 Mar 3;119(8):1158-60 - PubMed
  18. Chest. 2002 Oct;122(4):1471-7 - PubMed
  19. Chest. 2002 Dec;122(6):2230-3 - PubMed

Publication Types