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Korean J Thorac Cardiovasc Surg. 2020 Jun 05;53(3):144-146. doi: 10.5090/kjtcs.2020.53.3.144.

Aortic Valve-Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult.

The Korean journal of thoracic and cardiovascular surgery

Hong Ju Shin, Jae Seung Shin

Affiliations

  1. Department of Thoracic and Cardiovascular Surgery, Korea University Ansan Hospital, Korea University College of Medicine, Ansan, Korea.

PMID: 32551296 PMCID: PMC7287217 DOI: 10.5090/kjtcs.2020.53.3.144

Abstract

Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.

Copyright © The Korean Society for Thoracic and Cardiovascular Surgery. 2020. All right reserved.

Keywords: Aortic valve; Supravalvar aortic stenosis

Conflict of interest statement

Conflict of interest No potential conflict of interest relevant to this article

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