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Lee YH, Hsieh LC, Su CH, et al. Airway Management of the Deformed Trachea Using T-Tube Stents in Patients with Mucopolysaccharidosis Type IVA. Ann Otol Rhinol Laryngol. 2021;34894211032778doi: 10.1177/00034894211032778.
Lee, Y. H., Hsieh, L. C., Su, C. H., Lin, H. Y., Lin, S. P., & Lee, K. S. (2021). Airway Management of the Deformed Trachea Using T-Tube Stents in Patients with Mucopolysaccharidosis Type IVA. The Annals of otology, rhinology, and laryngology, 34894211032778. https://doi.org/10.1177/00034894211032778
Lee, Yi-Hao, et al. "Airway Management of the Deformed Trachea Using T-Tube Stents in Patients with Mucopolysaccharidosis Type IVA." The Annals of otology, rhinology, and laryngology vol. (2021): 34894211032778. doi: https://doi.org/10.1177/00034894211032778
Lee YH, Hsieh LC, Su CH, Lin HY, Lin SP, Lee KS. Airway Management of the Deformed Trachea Using T-Tube Stents in Patients with Mucopolysaccharidosis Type IVA. Ann Otol Rhinol Laryngol. 2021 Jul 20;34894211032778. doi: 10.1177/00034894211032778. Epub 2021 Jul 20. PMID: 34282634.
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Ann Otol Rhinol Laryngol. 2021 Jul 20;34894211032778. doi: 10.1177/00034894211032778. Epub 2021 Jul 20.

Airway Management of the Deformed Trachea Using T-Tube Stents in Patients with Mucopolysaccharidosis Type IVA.

The Annals of otology, rhinology, and laryngology

Yi-Hao Lee, Li-Chun Hsieh, Chin-Hui Su, Hsiang-Yu Lin, Shuan-Pei Lin, Kuo-Sheng Lee

Affiliations

  1. Department of Otorhinolaryngology-Head and Neck Surgery, MacKay Memorial Hospital, Taipei.
  2. Department of Audiology and Speech-Language Pathology, MacKay Medical College, New Taipei City.
  3. School of Medicine, Taipei Medical University, Taipei.
  4. Department of Medicine, MacKay Medical College, New Taipei City.
  5. Department of Pediatrics, MacKay Memorial Hospital, Taipei.
  6. MacKay Junior College of Medicine, Nursing and Management, Taipei.
  7. Department of Infant and Child Care, National Taipei University of Nursing and Health Sciences, Taipei.

PMID: 34282634 DOI: 10.1177/00034894211032778

Abstract

INTRODUCTION: Mucopolysaccharidosis (MPS) type IVA usually results in airway obstruction due to thoracic cage deformity and crowding of intrathoracic structures, causing tracheal compression by the tortuous innominate artery.

OBJECTIVES: To offer an alternative and effective method in dealing with the challenged deformity of the airway in patients with MPS type IVA.

METHODS: We present 3 patients with MPS type IVA who underwent airway stenting using Montgomery

RESULTS: All 3 patients had good outcomes during the follow-ups until present, despite the complication of granulation formation, which was resolved by revising the limbs of the T-tube.

CONCLUSIONS: T-tube stents placed below the vocal cord may restore airway patency and preserve laryngeal function, including respiration, phonation, and swallowing, in patients with MPS type IVA.

Keywords: Morquio A syndrome; T-tube; airway obstruction; innominate artery; mucopolysaccharidosis type IVA; tracheal deformity

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