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Assan F, Bottin L, Francès C, et al. Antiphospholipid-negative Sneddon's syndrome: A comprehensive overview of a rare entity. Ann Dermatol Venereol. 2021;doi: 10.1016/j.annder.2021.08.007.
Assan, F., Bottin, L., Francès, C., Moguelet, P., Tavolaro, S., Barbaud, A., de Zuttere, D., Alamowitch, S., & Chasset, F. (2021). Antiphospholipid-negative Sneddon's syndrome: A comprehensive overview of a rare entity. Annales de dermatologie et de venereologie, . https://doi.org/10.1016/j.annder.2021.08.007
Assan, F, et al. "Antiphospholipid-negative Sneddon's syndrome: A comprehensive overview of a rare entity." Annales de dermatologie et de venereologie vol. (2021). doi: https://doi.org/10.1016/j.annder.2021.08.007
Assan F, Bottin L, Francès C, Moguelet P, Tavolaro S, Barbaud A, de Zuttere D, Alamowitch S, Chasset F. Antiphospholipid-negative Sneddon's syndrome: A comprehensive overview of a rare entity. Ann Dermatol Venereol. 2021 Nov 02; doi: 10.1016/j.annder.2021.08.007. Epub 2021 Nov 02. PMID: 34740467.
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Ann Dermatol Venereol. 2021 Nov 02; doi: 10.1016/j.annder.2021.08.007. Epub 2021 Nov 02.

Antiphospholipid-negative Sneddon's syndrome: A comprehensive overview of a rare entity.

Annales de dermatologie et de venereologie

F Assan, L Bottin, C Francès, P Moguelet, S Tavolaro, A Barbaud, D de Zuttere, S Alamowitch, F Chasset

Affiliations

  1. Sorbonne University, Faculté de Médecine Sorbonne Université, AP-HP, Service de Dermatologie et Allergologie, Hôpital Tenon, 75020 Paris, France.
  2. Sorbonne University, Faculté de Médecine Sorbonne Université, AP-HP, Service de Neurologie, Hôpital Saint-Antoine, 75012 Paris, France.
  3. Sorbonne University, Faculté de Médecine Sorbonne Université, AP-HP, Service de Pathologie, Hôpital Tenon, 75020 Paris, France.
  4. Sorbonne University, Faculté de Médecine Sorbonne Université, AP-HP, Service de Radiologie, Hôpital Tenon, 75020 Paris, France.
  5. Service d'Explorations Fonctionnelles, Hôpital Franco-Britannique, 92300 Levallois-Perret, France.
  6. Sorbonne University, Faculté de Médecine Sorbonne Université, AP-HP, Service de Dermatologie et Allergologie, Hôpital Tenon, 75020 Paris, France. Electronic address: [email protected].

PMID: 34740467 DOI: 10.1016/j.annder.2021.08.007

Abstract

The term Sneddon's syndrome (SS) has been used since 1965 to describe a vasculopathy characterized by a combination of cerebrovascular disease with livedo racemosa. SS may be classified as antiphospholipid+ (aPL+) or antiphospholipid- (aPL-). Little is known about aPL- SS; in this review we describe the epidemiology and pathogenesis of aPL- SS, as well as the clinical and histologic features. We discuss recent findings in terms of neurologic and cardiac involvement. Moreover, differential diagnoses of conditions that may present with both livedo racemosa and stroke are discussed. Finally, we discuss real-life practical issues such as the initial investigations to be performed, long-term follow-up, and therapeutic management of aPL- SS patients.

Copyright © 2021 Elsevier Masson SAS. All rights reserved.

Keywords: Antiphospholipid; Cerebral infarction; Livedo racemosa; Sneddon's syndrome

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