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Insights Imaging. 2021 Oct 30;12(1):153. doi: 10.1186/s13244-021-01095-2.

Imaging of congenital lung diseases presenting in the adulthood: a pictorial review.

Insights into imaging

Gamze Durhan, Selin Ardali Duzgun, Meltem Gülsün Akpınar, Figen Demirkazık, Orhan Macit Arıyürek

Affiliations

  1. Department of Radiology, Faculty of Medicine, Hacettepe University, 06410, Ankara, Turkey. [email protected].
  2. Department of Radiology, Faculty of Medicine, Hacettepe University, 06410, Ankara, Turkey.

PMID: 34716817 PMCID: PMC8557233 DOI: 10.1186/s13244-021-01095-2

Abstract

Congenital lung diseases in adults are rare diseases that can present with symptoms or be detected incidentally. Familiarity with the imaging features of different types of congenital lung diseases helps both in correct diagnosis and management of these diseases. Congenital lung diseases in adults are classified into three main categories as bronchopulmonary anomalies, vascular anomalies, and combined bronchopulmonary and vascular anomalies. Contrast-enhanced computed tomography, especially 3D reconstructions, CT, or MR angiography, can show vascular anomalies in detail. The tracheobronchial tree, parenchymal changes, and possible complications can also be defined on chest CT, and new applications such as quantitative 3D reconstruction CT images, dual-energy CT (DECT) can be helpful in imaging parenchymal changes. In addition to the morphological assessment of the lungs, novel MRI techniques such as ultra-short echo time (UTE), arterial spin labeling (ASL), and phase-resolved functional lung (PREFUL) can provide functional information. This pictorial review aims to comprehensively define the radiological characteristics of each congenital lung disease in adults and to highlight differential diagnoses and possible complications of these diseases.

© 2021. The Author(s).

Keywords: Adults; Congenital lung diseases; Magnetic resonance imaging; Tomography (X-ray computed)

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